Idiopathic pulmonary haemosiderosis: an unusual case of anaemia with pulmonary involvement

نویسندگان

چکیده

Idiopathic pulmonary haemosiderosis is a rare disorder, with recurrent life-threatening alveolar haemorrhages and chronic lung parenchymal changes. It associated triad of haemoptysis, iron deficiency anaemia, diffuse infiltrates. Although most cases are idiopathic, secondary linked to known diseases has also been observed. Most the remain undiagnosed because disease very low on list differentials. There no specified age for disease. The present study reports an adolescent female patient who presented microcytic anaemia bilateral infiltrates National Institute Child Health (NICH), Karachi, tertiary care hospital. She was diagnosed after ruling out other possibilities. Keywords: Pulmonary haemosiderosis, Alveolar haemorrhages, Lung disease, hypoventilation syndrome.

برای دانلود باید عضویت طلایی داشته باشید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Idiopathic pulmonary haemosiderosis with mineralizing pulmonary elastosis: A case report

INTRODUCTION Idiopathic pulmonary haemosiderosis characterized by repeated episodes of intra-alveolar haemorrhage is rare in adults and has a relatively benign course compared to cases seen in children. CASE PRESENTATION The case presented here is of an adult man with idiopathic pulmonary haemosiderosis with mineralizing pulmonary elastosis. CONCLUSION Pathologists are generally not familia...

متن کامل

Idiopathic pulmonary haemosiderosis revisited.

Idiopathic pulmonary haemosiderosis is a rare cause of diffuse alveolar haemorrhage of unknown aetiology. It occurs most frequently in children, has a variable natural history with repetitive episodes of diffuse alveolar haemorrhage, and has been reported to have a high mortality. Many patients develop iron deficiency anaemia secondary to deposition of haemosiderin iron in the alveoli. Examinat...

متن کامل

Idiopathic pulmonary haemosiderosis in an adult.

We report a very, rare case of idiopathic pulmonary haemosiderosis (IPH) occurring in a 68 yr old patient. Following alveolar haemorrhage onset, the diagnosis was obtained by a process of elimination, after clinical, endoscopic, cytohistological and laboratory investigations. The immunoglobulin G directed against myeloperoxidase antigen (C-ANCA), which was detected, can be regarded as indicativ...

متن کامل

A Case of Idiopathic Pulmonary Haemosiderosis with Myocarditis.

Idiopathic pulmonary haemosiderosis is a not uncommon condition characterized clinically by anaemia, haemoptysis, and radiological changes in the luing fields. It was first described by Ceelen (1931), and the clinical and pathological findings of the disease have been fully reviewed by Wyllie, Sheldon, Bodian and Barlow (1948). This case is presented because of the association of myocarditis wi...

متن کامل

Idiopathic pulmonary haemosiderosis in children.

Idiopathic pulmonary haemosiderosis (IPH) was first described by Virchow in 1865 as 'brown lung induration'. In 1931 Ceelen reported the necropsy findings in 2 children. The clinical picture in association with radiological and pathological findings was reported by Waldenstrom (1944), and Wyllie et al. (1948) reviewed 24 cases in children. Nearly 200 have since been reported. In the past 5 year...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

ژورنال

عنوان ژورنال: Journal of Pakistan Medical Association

سال: 2023

ISSN: ['0030-9982']

DOI: https://doi.org/10.47391/jpma.7323